Xanthoma disseminatum with extensive koebnerization associated with familial hypertriglyceridemia
نویسندگان
چکیده
FHTG: familial hypertriglyceridemia HDL: high-density lipoprotein LCH: Langerhan’s cell histiocytosis LDL: low-density lipoprotein VLDL: very low-density lipoprotein XD: xanthoma disseminatum INTRODUCTION Xanthoma disseminatum (XD) is a rare subtype of non-Langerhan’s cell histiocytosis (non-LCH). To date, just greater than 100 cases of XD have been reported; however, association with hyperlipidemia is extremely rare. We present a unique case of XD associated with familial hypertriglyceridemia (FHTG). Additionally, the patient had an extensive K€ oebner response.
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Xanthoma disseminatum: case report and mini-review of the literature.
Xanthoma disseminatum is a non-familial disorder of non-Langerhans cell origin or a class II histiocytosis with unknown etiology, with just over 100 cases reported in the literature. Because of the rarity of this disease, there is no established treatment. We studied clinical manifestations and different treatments of xanthoma disseminatum from a series of cases, including our own patient. We s...
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